Ether phospholipid synthesis occurs in?
Peroxisome
Very long chain fatty acid oxidation occurs in?
Peroxisome
Fatty acids are transported into Mitochondria by?
Carnitine acyltranslocase
Beta oxidation of odd chain fatty acids produce?
Acetyl CoA + Propionyl CoA
Beta oxidation of palmitic acid?
129 ATP net, 96 ATP from citric acid cycle
No of ATP by one turn of beta oxidation of fatty acid?
5
Refsum Disease?
X linked Adrenoleukodystrophy?
Defect in peroxisomal beta oxidation
Fatty acid oxidation presents as?
Hyperammonemia
Refsum disease is due to defect in?
Beta oxidation of fatty acid
