Oxidation Of Fatty Acids – Lipids – Biochemistry

Ether phospholipid synthesis occurs in?
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Peroxisome

Very long chain fatty acid oxidation occurs in?
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Peroxisome

Fatty acids are transported into Mitochondria by?
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Carnitine acyltranslocase

Beta oxidation of odd chain fatty acids produce?
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Acetyl CoA + Propionyl CoA

Beta oxidation of palmitic acid?
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129 ATP net, 96 ATP from citric acid cycle

No of ATP by one turn of beta oxidation of fatty acid?
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5

Refsum Disease?
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X linked Adrenoleukodystrophy?
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Defect in peroxisomal beta oxidation

Fatty acid oxidation presents as?
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Hyperammonemia

Refsum disease is due to defect in?
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Beta oxidation of fatty acid
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